Long earLong ear is a condition in which the ears are unusually long from top to bottom. This is defined as the median longitudinal ear length being over 2 SD from the mean external ear length.ConditionsLong ear is seen in: Cohen-Gibson syndrome Congenital disorder of glycosylation, type Iw, autosomal dominant Diets-Jongmans syndrome Faundes-Banka syndrome Schinzel phocomelia syndrome