Heterodimeric amino-acid transporter


Heterodimeric amino-acid transporters are a family of transport proteins that facilitate the transport of certain amino acids across cell membranes. Each comprises a light and a heavy protein subunit. Transport activity happens in the light.
The following table lists the members of this family:
Transport systemLight subunitHeavy subunitTissue distributionSubstratesAffinitySodium dependenceDisease linkage
LLAT1 4F2hc kidney, liver, intestine, brain, heart lung, blood–brain barrierlarge neutral amino acids, thyroid hormonesmicromolarno
LLAT2 4F2hc kidney, intestine, brain, liver, muscle, heart, lungsmaller neutral amino acidsmillimolarno
y+Ly+LAT1 4F2hc kidney, intestine, lung, erythrocytes, leukocyteslarge neutral amino acids, dibasic amino acid exchangemicromolaryesLysinuric protein intolerance
y+Ly+LAT2 4F2hc brain, intestine, heart, kidney, lung, liverneutral amino acids, dibasic amino acid exchange, glutamine/arginine exchangemillimolaryes
xcxCT 4F2hc macrophages, liver, kidney, brainglutamine/cystine exchangeno
ascascAT1 4F2hc brain, lung, small intestine, kidneysmall neutral amino acidsno
b0,+b0,+AT1 rBAT kidney, intestine, brainneutral/dibasic amino acidsnoCystinuria type I