Chapel Hill Consensus Conference
The Chapel Hill Consensus Conferences are a pair of international conferences which addressed the need of standardized classification system for systemic vasculitides.
2012 Revised International Chapel Hill Consensus Conference Nomenclature of Vasculitides
| Classification Group | Diseases |
| Large-vessel vasculitis | Takayasu's arteritis ; Giant-cell arteritis |
| Medium-vessel vasculitis | Polyarteritis nodosa, Kawasaki disease |
| Small vessel vasculitis | ANCA-associated vasculitis ; Immune complex SVV |
| Variable vessel vasculitis | Behcet's disease ; Cogan's syndrome |
| Single Organ Vasculitis | Cutaneous leukocytoclastic angiitis; cutaneous arteritis; primary central nervous system vasculitis; isolated aortitis; others |
| Vasculitis associated with systemic disease | Lupus vasculitis; Rheumatoid vasculitis; Sarcoid vasculitis; others |
| Vasculitis associated with probable etiology | Hepatitis C virus-associated cryoglobulinemic vasculitis; Hepatitis B virus-associated vasculitis; Syphilis-associated aortitis; Drug-associated immune complex vasculitis; Cancer-associated vasculitis; others |